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A syndrome now known as Ehlers–Danlos, comprising laxity and fragility of the skin associated with hypermobility of the large joints, was published in 1892 by Tschernogobow. Ehlers–Danlos type VIIA is an extremely rare form of the syndrome. While the UK-based Ehlers–Danlos Support Group ® recommends that the surgical management of patients with Ehlers–Danlos VIIA should be carried out in conjunction...