Purpose A peripapillary detachment in pathologic myopia (PDPM) appears as a yellowish-orange lesion around the optic disc in highly myopic eyes. We report a case in which a macular retinal detachment (RD) accompanied a PDPM. Method A case report was used in this study. Results The right eye in a 48-year-old man showed a macular RD and a PDPM. Fluorescein fundus angiography showed no dye leakage, suggestive of an optic pit within the optic disc. Optical coherence tomography (OCT) examination revealed that there was a full-thickness tissue defect in the retina overlying PDPM, the vitreous cavity was connected to PDPM through this defect, and the PDPM was continuous with the RD through the subretinal path at the conus area. Conclusions These findings suggest that this eye had a macular RD associated with a PDPM, and eyes with a PDPM might be at risk of developing macular RD.