Purpose
Borderline ovarian tumors tend to be uncommon in 20 years and below 20 years of age. With exclusion of dysgenetic gonads, primary amenorrhea is less likely to be associated with ovarian malignancies and more so in borderline tumors.
Methods
Here we would like to present a case of 20 years old with primary amenorrhea incidentally diagnosed with ovarian mass.
Results
She underwent laparotomy and intraoperatively had bilateral ovarian mass with uterus didelphys. Left salpingo oophorectomy and right ovarian cystectomy were done. Histopathology showed borderline serous ovarian tumor. Postoperative secondary lymphangiectasia was diagnosed and resolved spontaneously.
Conclusion
Twenty-year-old normal karyotype female having primary amenorrhea in association with an unusual combination of lateral and vertical fusion defects, nonfunctioning endometrium, and the coexistence of borderline ovarian tumor per se in such young patient proved a therapeutic challenge. Thorough search of the literature showed no such case being reported worldwide.