We report a rare case of right coronary artery–coronary sinus fistula successfully closed through coronary sinus in the second operation following identification of distal branches of the coronary artery. At nine months follow-up, patient is asymptomatic with no recurrence of cardiac murmur. Repeat coronary angiography at one year showed no connection between right coronary artery and coronary sinus. This case report highlights the difficulties in angiographic techniques, identification and interpretation of anatomy of these rare malformations. It also demonstrates the hazards of simple ligation of these anomalous vessels without first understanding the anatomy of the regional coronary circulation. A brief review of literature on coronary artery fistula will be presented.