PURPOSE:To report a patient who had concomitant idiopathic polypoidal choroidal vasculopathy and sickle cell retinopathy.METHOD:Case report. A 46-year-old black woman presented with sudden onset of ''blurring'' in the left eye. Her ocular history was unremarkable, and her medical history was relevant for sickle cell disease with yearly episodes of sickle cell crises.RESULTS:Both eyes had evidence of idiopathic polypoidal choroidal vasculopathy and peripheral retinal neovascularization secondary to sickle cell disease. The left eye had hemorrhagic retinal pigment epithelial detachments secondary to idiopathic polypoidal choroidal vasculopathy.CONCLUSION:We present this case as an example of concomitant sickle cell retinopathy and idiopathic polypoidal choroidal vasculopathy. We are unaware of previous reports with these findings.