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Dowling Degos disease (DDD) is a rare autosomal dominant genodermatosis characterized by acquired, slowly progressive reticulated pigmented lesions primarily involving flexural skin areas. Mutations in KRT5, POGLUT‐1 and POFUT‐1 genes have been associated with DDD, and loss‐of‐function mutations in PSENEN, a subunit of the gamma‐secretase complex, were found in patients presenting with DDD or DDD...